A rare case of porokeratosis mibelli in 3-year-old boy

Introduction: Porokeratosis mibelli is a rare, chronic, and slowly progressive genodermatotic characterized by abnormality of keratinization. The clinical manifestations are hyperkeratotic papules or plaques surrounded thread-like elevated border that widens centrifugally. Rarity this case means the science behind it underdeveloped. Thus, we present as an educational vehicle to further develop body knowledge surrounding disease.Case report: We reported 3 years old boy, suspect porokeratosis mibelli. His mother complained few reddish spots patches sometimes itchy, healed into white brownish with atrophic centers in last 5 months before admission. Physical examination: lesions on back, waist, left side buttock, back neck, lateral upper arm. Hypopigmented hyperpigmented centers, erythematous central erosion were found. No internal organs laboratory findings. Histopathology examination showed epidermis contains invagination rete malpighia filled keratin. Slightly thinned stratum germinativum corneum basket weave pattern. Topical therapy 1% 5-fluorourasil cream twice daily mild improvement after 10 days.Conclusion: Although examinations patient did not fit criteria mibelli, however, results histopathology supported diagnosis. Treatment slow but healing